Neurology - Research & Surgery

Open Access ISSN: 2641-4333

Abstract


Fahr's Syndrome; True Clinical Orphan: Experience of A Young Togolese and Review of The Literature

Authors: Agba Léhleng, Kumako V. Kodzo, Dagbe Massagba, Kombate Damelan, Anayo K. Nyinèvi, Guinhouya K. Mensah, Assogba Komi, Belo Mofou, Balogou Koffi Agnon.

Background: There is no clinical sign to suspect Fahr's syndrome when examining the patient.

Objective: To report the experience of a Togolese 32-year-old reseller and do a review of the literature.

Case Presentation: A 32-year-old Togolese woman, reseller, has long wandered from consultation to consultation for headaches and psychiatric symptoms such as insomnia and nightmares. When she was received in neurological consultation, the imaging revealed symmetrical calcifications of the basal ganglia and the biology confirmed an endocrinopathy which is hypoparathyroidism.

Conclusion: This case study underlines that only imaging allows to suspect Fahr’s syndrome. However, imaging does not allow to make a difference with Fahr's disease. The peculiarity of Fahr’s syndrome is its frequent association with an underlying pathology that is most often hypoparathyroidism.

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