Double aortic arch is a rare congenital malformation. It is the most common cause of symptomatic complete vascular ring. Its signs are non-specific, making diagnosis difficult.

We retrospectively analysed 3 files of patients hospitalised at the Albert Royer Hospital for double aortic arch during the year 2020. We collected data concerning the circumstances of discovery, the time to diagnosis, the clinical signs and the therapeutic modalities. The mean age at diagnosis was 8 months. Clinical signs at the time of diagnosis were dominated by respiratory distress and stridor. The interrogation revealed recurrent respiratory infections. All 3 patients underwent surgical management.