Introduction: A caudal appendix is a rare congenital malformation of the median or paramedian diverticulum type located mainly in the lumbosacral region, of soft consistency, exceptionally provided with an axial skeleton and covered with skin often of normal appearance and simulating a tail.

Patients: We report the cases of three female patients including two infants aged 4 months and 12 months and an adult aged 35 years. The infants presented caudal appendages located at the atypical breech surface associated with a right cephalocele and the adults had a caudal appendage 11 cm long located at the lumbosacral level 2 cm from the midline on the right. Clinical examination noted one lesion in the first infant and three caudal appendages in the second. The neurological examination was normal. The adult patient did not present any associated clinical
malformation. The CT scan noted cranial dysraphism in the form of intra-orbital meningocele associated with shizencephaly for both infants.

Conclusion: Caudal appendages are rare and represent markers of dysraphism, which can be cranial or caudal. Their presence requires systematic research through medical imaging examinations.